Angiomatosis

Classification	D MeSH: D000798; SNOMED CT: 205562004;
External resources	eMedicine: article/1051846;

Angiomatosis
Angiomatosis
	Skin angiomatosis
Specialty	Cardiology

Angiomatosis is a non-neoplastic condition^[1] characterised by nests of proliferating capillaries arranged in a lobular pattern, displacing adjacent muscle and fat.^[2] It consists of many angiomas.^[3]

These tend to be cavernous hemangiomas, which are sharply defined, sponge-like tumors composed of large, dilated, cavernous vascular spaces.^{[citation needed]}

Presentation[]

Associated[]

They often appear in:

Von Hippel-Lindau disease: It can be associated with Von Hippel-Lindau Disease and is a rare genetic multi system disorder characterized by the abnormal growth of tumours in the body. Symptoms may include headaches, problems with balance and walking, dizziness, weakness of the limbs, vision problems and high blood pressure.^[4]
Bacillary angiomatosis
Klippel-Trenaunay-Weber syndrome
Sturge-Weber syndrome

Histology[]

It is a vascular malformation wherein blood vessels proliferate along with accompanying mature fat and fibrous tissue, lymphatics and sometimes nerves.^[2] They may involve skin, subcutaneous tissue, skeletal muscle and occasionally bone.^[2]

Diagnosis[]

Prognosis[]

Prognosis depends on the size and location of the tumour, untreated angiomatosis may lead to blindness and/ or permanent brain damage. Death may occur, with complications in the kidney or brain.^[4]

References[]

^ Angiomatosis at the US National Library of Medicine Medical Subject Headings (MeSH)
^ Jump up to: ^a ^b ^c Howat, AJ; Campbell, PE (October 1987). "Angiomatosis: a vascular malformation of infancy and childhood. Report of 17 cases". Pathology. 19 (4): 377–82. doi:10.3109/00313028709103887. PMID 3444663.
^ "angiomatosis" at Dorland's Medical Dictionary
^ Jump up to: ^a ^b "Von Hippel-Lindau Disease (VHL) Information Page". www.ninds.nih.gov. National Institute of Neurological Disorders and Stroke.

External links[]

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[1] Angiomatosis at the US National Library of Medicine Medical Subject Headings (MeSH)

[pmd3444663-2] Jump up to: ^a ^b ^c Howat, AJ; Campbell, PE (October 1987). "Angiomatosis: a vascular malformation of infancy and childhood. Report of 17 cases". Pathology. 19 (4): 377–82. doi:10.3109/00313028709103887. PMID 3444663.

[3] "angiomatosis" at Dorland's Medical Dictionary

[NINDS_Info_Page-4] Jump up to: ^a ^b "Von Hippel-Lindau Disease (VHL) Information Page". www.ninds.nih.gov. National Institute of Neurological Disorders and Stroke.

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show v t Phakomatosis
Angiomatosis	Sturge–Weber syndrome Von Hippel–Lindau disease
Hamartoma	Tuberous sclerosis Hypothalamic hamartoma (Pallister–Hall syndrome) Multiple hamartoma syndrome Proteus syndrome Cowden syndrome Bannayan–Riley–Ruvalcaba syndrome Lhermitte–Duclos disease
Neurofibromatosis	Type I Type II
Other	Abdallat–Davis–Farrage syndrome Ataxia telangiectasia Incontinentia pigmenti Peutz–Jeghers syndrome Encephalocraniocutaneous lipomatosis